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E712026

Non-billable

Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

Clinical Notes

    From E70-E88
    • Androgen insensitivity syndrome (E34.5-)
    • Congenital adrenal hyperplasia (E25.0)
    • Hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan syndrome (Q87.4-)
    • 5-alpha-reductase deficiency (E29.1)
    From E00-E89
    • Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

    Frequently Asked Questions

    Code Hierarchy
    E71
    Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
    Maple-syrup-urine disease
    Other disorders of branched-chain amino-acid metabolism
    Disorder of branched-chain amino-acid metabolism, unspecified
    ...fatty-acid metabolism
    ...carnitine metabolism
    Peroxisomal disorders

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    Related MS-DRGs
    61,940 Medicare hospitalizations across 1 DRG for codes in E71

    Top DRGs associated with codes in this category:

    642INBORN AND OTHER DISORDERS OF METABOLISM61,940
    Official Guidelines
    Chapter 4: Endocrine, Nutritional, and Metabolic Diseases

    Official coding guidelines for E00-E89

    Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism - ICD-10 Code E71 | FindICD10