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E752026

Non-billable

Disorders of sphingolipid metabolism and other lipid storage disorders

Clinical Notes

  • Mucolipidosis, types I-III (E77.0-E77.1)
  • Refsum's disease (G60.1)
From E70-E88
  • Androgen insensitivity syndrome (E34.5-)
  • Congenital adrenal hyperplasia (E25.0)
  • Hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
From E00-E89
  • Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Frequently Asked Questions

Code Hierarchy
Metabolic disorders (E70-E88)
Disorders of aromatic amino-acid metabolism
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
Other disorders of amino-acid metabolism
Lactose intolerance
Other disorders of carbohydrate metabolism
E75
Disorders of sphingolipid metabolism and other lipid storage disorders
GM2 gangliosidosis
Other and unspecified gangliosidosis
Other sphingolipidosis
Sphingolipidosis, unspecified
Neuronal ceroid lipofuscinosis
Other lipid storage disorders
Lipid storage disorder, unspecified
Disorders of glycosaminoglycan metabolism
Disorders of glycoprotein metabolism
Disorders of lipoprotein metabolism and other lipidemias
Disorders of purine and pyrimidine metabolism
Disorders of porphyrin and bilirubin metabolism
Disorders of mineral metabolism
Cystic fibrosis
Amyloidosis
Volume depletion
Other disorders of fluid, electrolyte and acid-base balance
Other and unspecified metabolic disorders

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Related MS-DRGs
591,390 Medicare hospitalizations across 3 DRGs for codes in E75

Top DRGs associated with codes in this category:

057DEGENERATIVE NERVOUS SYSTEM DISORDERS WITHOUT MCC370,510
056DEGENERATIVE NERVOUS SYSTEM DISORDERS WITH MCC201,320
642INBORN AND OTHER DISORDERS OF METABOLISM19,560
Official Guidelines
Chapter 4: Endocrine, Nutritional, and Metabolic Diseases

Official coding guidelines for E00-E89

Disorders of sphingolipid metabolism and other lipid storage disorders - ICD-10 Code E75 | FindICD10