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E762026

Non-billable

Disorders of glycosaminoglycan metabolism

Clinical Notes

    From E70-E88
    • Androgen insensitivity syndrome (E34.5-)
    • Congenital adrenal hyperplasia (E25.0)
    • Hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan syndrome (Q87.4-)
    • 5-alpha-reductase deficiency (E29.1)
    From E00-E89
    • Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

    Frequently Asked Questions

    Code Hierarchy
    Metabolic disorders (E70-E88)
    Disorders of aromatic amino-acid metabolism
    Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
    Other disorders of amino-acid metabolism
    Lactose intolerance
    Other disorders of carbohydrate metabolism
    Disorders of sphingolipid metabolism and other lipid storage disorders
    E76
    Disorders of glycosaminoglycan metabolism
    Mucopolysaccharidosis, type I
    Mucopolysaccharidosis, type II
    Other mucopolysaccharidoses
    Mucopolysaccharidosis, unspecified
    Other disorders of glucosaminoglycan metabolism
    Glucosaminoglycan metabolism disorder, unspecified
    Disorders of glycoprotein metabolism
    Disorders of lipoprotein metabolism and other lipidemias
    Disorders of purine and pyrimidine metabolism
    Disorders of porphyrin and bilirubin metabolism
    Disorders of mineral metabolism
    Cystic fibrosis
    Amyloidosis
    Volume depletion
    Other disorders of fluid, electrolyte and acid-base balance
    Other and unspecified metabolic disorders

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    Related MS-DRGs
    19,560 Medicare hospitalizations across 1 DRG for codes in E76

    Top DRGs associated with codes in this category:

    642INBORN AND OTHER DISORDERS OF METABOLISM19,560
    Official Guidelines
    Chapter 4: Endocrine, Nutritional, and Metabolic Diseases

    Official coding guidelines for E00-E89