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E802026

Non-billable

Disorders of porphyrin and bilirubin metabolism

Clinical Notes

    From E70-E88
    • Androgen insensitivity syndrome (E34.5-)
    • Congenital adrenal hyperplasia (E25.0)
    • Hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan syndrome (Q87.4-)
    • 5-alpha-reductase deficiency (E29.1)
    From E00-E89
    • Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

    Frequently Asked Questions

    Code Hierarchy
    Metabolic disorders (E70-E88)
    Disorders of aromatic amino-acid metabolism
    Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
    Other disorders of amino-acid metabolism
    Lactose intolerance
    Other disorders of carbohydrate metabolism
    Disorders of sphingolipid metabolism and other lipid storage disorders
    Disorders of glycosaminoglycan metabolism
    Disorders of glycoprotein metabolism
    Disorders of lipoprotein metabolism and other lipidemias
    Disorders of purine and pyrimidine metabolism
    E80
    Disorders of porphyrin and bilirubin metabolism
    Hereditary erythropoietic porphyria
    Porphyria cutanea tarda
    Other and unspecified porphyria
    Defects of catalase and peroxidase
    Gilbert syndrome
    Crigler-Najjar syndrome
    Other disorders of bilirubin metabolism
    Disorder of bilirubin metabolism, unspecified
    Disorders of mineral metabolism
    Cystic fibrosis
    Amyloidosis
    Volume depletion
    Other disorders of fluid, electrolyte and acid-base balance
    Other and unspecified metabolic disorders

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    Related MS-DRGs
    124,868 Medicare hospitalizations across 4 DRGs for codes in E80

    Top DRGs associated with codes in this category:

    441DISORDERS OF LIVER EXCEPT MALIGNANCY, CIRRHOSIS OR ALCOHOLIC HEPATITIS WITH MCC66,376
    442DISORDERS OF LIVER EXCEPT MALIGNANCY, CIRRHOSIS OR ALCOHOLIC HEPATITIS WITH CC43,400
    642INBORN AND OTHER DISORDERS OF METABOLISM9,780
    443DISORDERS OF LIVER EXCEPT MALIGNANCY, CIRRHOSIS OR ALCOHOLIC HEPATITIS WITHOUT CC/MCC5,312
    Official Guidelines
    Chapter 4: Endocrine, Nutritional, and Metabolic Diseases

    Official coding guidelines for E00-E89

    Disorders of porphyrin and bilirubin metabolism - ICD-10 Code E80 | FindICD10