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E842026

Non-billable

Cystic fibrosis

Clinical Notes

    From E70-E88
    • Androgen insensitivity syndrome (E34.5-)
    • Congenital adrenal hyperplasia (E25.0)
    • Hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan syndrome (Q87.4-)
    • 5-alpha-reductase deficiency (E29.1)
    From E00-E89
    • Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

    Frequently Asked Questions

    Code Hierarchy
    Metabolic disorders (E70-E88)
    Disorders of aromatic amino-acid metabolism
    Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
    Other disorders of amino-acid metabolism
    Lactose intolerance
    Other disorders of carbohydrate metabolism
    Disorders of sphingolipid metabolism and other lipid storage disorders
    Disorders of glycosaminoglycan metabolism
    Disorders of glycoprotein metabolism
    Disorders of lipoprotein metabolism and other lipidemias
    Disorders of purine and pyrimidine metabolism
    Disorders of porphyrin and bilirubin metabolism
    Disorders of mineral metabolism
    E84
    Cystic fibrosis
    ...pulmonary manifestations
    ...intestinal manifestations
    ...other manifestations
    ...fibrosis, unspecified
    Amyloidosis
    Volume depletion
    Other disorders of fluid, electrolyte and acid-base balance
    Other and unspecified metabolic disorders

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    Related MS-DRGs
    555,195 Medicare hospitalizations across 5 DRGs for codes in E84

    Top DRGs associated with codes in this category:

    177RESPIRATORY INFECTIONS AND INFLAMMATIONS WITH MCC168,969
    640MISCELLANEOUS DISORDERS OF NUTRITION, METABOLISM, FLUIDS AND ELECTROLYTES WITH MCC147,308
    641MISCELLANEOUS DISORDERS OF NUTRITION, METABOLISM, FLUIDS AND ELECTROLYTES WITHOUT MCC130,638
    178RESPIRATORY INFECTIONS AND INFLAMMATIONS WITH CC40,367
    394OTHER DIGESTIVE SYSTEM DIAGNOSES WITH CC30,250
    Official Guidelines
    Chapter 4: Endocrine, Nutritional, and Metabolic Diseases

    Official coding guidelines for E00-E89

    Cystic fibrosis - ICD-10-CM Code E84 2026 | FindICD10